Introduction
The purpose of these clinical guidelines for cystic fibrosis (CF) is to ensure standardised care for children with CF looked after at Royal Brompton & Harefield NHS Foundation Trust and district general hospitals on a network care basis. They should be used as a guide only. Royal Brompton Hospital is a specialist CF centre as defined by the specialist commissioners, NHS England.
Viewing the clinical guidelines
Our clinical guidelines can be viewed by chapter and appendix via PDF, in full via PDF or downloaded in full via an app
By chapter and appendix
- What's new in the 8th edition?
- 1. Introduction
- 2. Our multidisciplinary team
- 3. How the service runs
- 4. Admission to hospital
- 5. Making the diagnosis
- 6. Respiratory care
- 7. Gastrointestinal and nutritional care
- 8. Other non-pulmonary complications of CF
- 9. Transplant assessment
- 10. Miscellaneous
- 11. Drug formulary
- Appendix 1 - Transition integrated care pathway
- Appendix 2 - Risks of getting P. aeruginosa from the environment
- Appendix 3 - Cystic fibrosis pre-admission plan
- Appendix 4 - Paediatric cystic fibrosis intravenous aminoglycoside consent form
- Appendix 5 - Drug response assessement testing
- Appendix 6 - Guide for parents starting a child on nebuliser therapy
- Appendix 7 - Physiotherapy device & nebuliser cleaning
- Appendix 8 - Sputum induction protocol
- Appendix 9 - Gastrostomy care
- Appendix 10 - Gene variants' nomenclature
- Appendix 11 - Hot weather advice
- Appendix 12 - Travel letters
- Appendix 13 - Safeguarding children pathway
- Appendix 14 - Social security benefits
- Appendix 15 - NHSE commissioning medicines for children in specialised services
- Appendix 16 - Payment by results guidance 2019-2020
- Appendix 17 - Nomogram for body surface area
- Appendix 18 - Cystic fibrosis Trust consensus documents, factsheets and leaflets
- Appendix 19 - Useful telephone numbers
Download full PDF
Download the clinical guidelines in full here.
View through an app
These clinical guidelines can be downloaded onto your smartphone. Follow these instructions to download the app:
- Open the App Store app on your device
- Select the search icon, located on the bottom right of your screen
- Enter 'Brompton Cystic Fibrosis guide' into the search bar (there will only be one app available under this search)
- Select 'Get'
- Select 'Yes' to confirm your download.
The app will now download and then appear on your device for you to use. Ensure you enter your login details to access the contents of these guidelines.
- Open the Google play app on your device
- Select the search icon
- Enter 'Brompton Cystic Fibrosis guide' into the search bar (there will only be one app available under this search)
- Select 'Download'
- Select 'Yes' to confirm your download.
The app will now download and then appear on your device for you to use. Ensure you enter your login details to access the contents of these guidelines.